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<article article-type="research-article" dtd-version="1.3" xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance" xml:lang="ru"><front><journal-meta><journal-id journal-id-type="publisher-id">psychiatry</journal-id><journal-title-group><journal-title xml:lang="ru">ПСИХИАТРИЯ</journal-title><trans-title-group xml:lang="en"><trans-title>Psychiatry (Moscow) (Psikhiatriya)</trans-title></trans-title-group></journal-title-group><issn pub-type="ppub">1683-8319</issn><issn pub-type="epub">2618-6667</issn><publisher><publisher-name>FSBSI “The Mental Health Research Centre”;   LLC «Publisher «MIA»</publisher-name></publisher></journal-meta><article-meta><article-id pub-id-type="doi">10.30629/2618-6667-2022-20-1-6-16</article-id><article-id custom-type="elpub" pub-id-type="custom">psychiatry-774</article-id><article-categories><subj-group subj-group-type="heading"><subject>Research Article</subject></subj-group><subj-group subj-group-type="section-heading" xml:lang="ru"><subject>ПСИХОПАТОЛОГИЯ, КЛИНИЧЕСКАЯ И БИОЛОГИЧЕСКАЯ ПСИХИАТРИЯ</subject></subj-group><subj-group subj-group-type="section-heading" xml:lang="en"><subject>PSYCHOPATHOLOGY, CLINICAL AND BIOLOGICAL PSYCHIATRY</subject></subj-group></article-categories><title-group><article-title>Кататония (актуальные проблемы психопатологии и клинической систематики)</article-title><trans-title-group xml:lang="en"><trans-title>Catatonia (Actual Problems of Psychopatology and Clinical Systematics)</trans-title></trans-title-group></title-group><contrib-group><contrib contrib-type="author" corresp="yes"><contrib-id contrib-id-type="orcid">https://orcid.org/0000-0003-2737-3432</contrib-id><name-alternatives><name name-style="eastern" xml:lang="ru"><surname>Смулевич</surname><given-names>А. Б.</given-names></name><name name-style="western" xml:lang="en"><surname>Smulevich</surname><given-names>A. B.</given-names></name></name-alternatives><bio xml:lang="ru"><p>Анатолий Болеславович Смулевич, академик РАН, доктор медицинских наук, заведующий отделом по изучению пограничной психической патологии и психосоматических расстройств, ФГБНУ Научный центр психического здоровья; заведующий кафедрой психиатрии и психосоматики, ИКМ ФГАОУ ВО Первый МГМУ им. И.М. Сеченова Минздрава России (Сеченовский Университет)</p><p>Москва</p></bio><bio xml:lang="en"><p>Anatoly B. Smulevich, Academician of RAS, Professor, Dr. of Sci. (Med.), Head of Department, FSBSI Mental Health Research Centre, Head of Psychiatry and Psychosomatics Department, I.M. Sechenov First Moscow State Medical University of the Ministry of Health of the Russian Federation (Sechenov University)</p><p>Moscow</p></bio><email xlink:type="simple">absmulevich@list.ru</email><xref ref-type="aff" rid="aff-1"/></contrib><contrib contrib-type="author" corresp="yes"><contrib-id contrib-id-type="orcid">https://orcid.org/0000-0001-5148-3864</contrib-id><name-alternatives><name name-style="eastern" xml:lang="ru"><surname>Клюшник</surname><given-names>Т. П.</given-names></name><name name-style="western" xml:lang="en"><surname>Klyushnik</surname><given-names>T. P.</given-names></name></name-alternatives><bio xml:lang="ru"><p>Татьяна Павловна Клюшник, профессор, доктор медицинских наук, заведующая лаборатории нейроиммунологии</p><p>Москва</p></bio><bio xml:lang="en"><p>Tatyana P. Klyushnik, Professor, Dr. of Sci. (Med.), Head of the Laboratory of Neuroimmunology, director</p><p>Moscow</p></bio><email xlink:type="simple">klushnik2004@mail.ru</email><xref ref-type="aff" rid="aff-2"/></contrib><contrib contrib-type="author" corresp="yes"><contrib-id contrib-id-type="orcid">https://orcid.org/0000-0002-6563-9169</contrib-id><name-alternatives><name name-style="eastern" xml:lang="ru"><surname>Борисова</surname><given-names>П. О.</given-names></name><name name-style="western" xml:lang="en"><surname>Borisova</surname><given-names>P. O.</given-names></name></name-alternatives><bio xml:lang="ru"><p>Полина Олеговна Борисова, младший научный сотрудник</p><p>Москва</p></bio><bio xml:lang="en"><p>Polina O. Borisova, Junior Researcher</p><p>Moscow</p></bio><email xlink:type="simple">bori.pauline@gmail.com</email><xref ref-type="aff" rid="aff-2"/></contrib><contrib contrib-type="author" corresp="yes"><contrib-id contrib-id-type="orcid">https://orcid.org/0000-0002-7183-1536</contrib-id><name-alternatives><name name-style="eastern" xml:lang="ru"><surname>Лобанова</surname><given-names>В. М.</given-names></name><name name-style="western" xml:lang="en"><surname>Lobanova</surname><given-names>V. M.</given-names></name></name-alternatives><bio xml:lang="ru"><p>Вероника Маратовна Лобанова, младший научный сотрудник</p><p>Москва</p></bio><bio xml:lang="en"><p>Veronika M. Lobanova, Junior Researcher</p><p>Moscow</p></bio><email xlink:type="simple">l.o.b.a.n.o.v.a.n.i.k.a@gmail.com</email><xref ref-type="aff" rid="aff-2"/></contrib><contrib contrib-type="author" corresp="yes"><contrib-id contrib-id-type="orcid">https://orcid.org/0000-0001-6605-4851</contrib-id><name-alternatives><name name-style="eastern" xml:lang="ru"><surname>Воронова</surname><given-names>Е. И.</given-names></name><name name-style="western" xml:lang="en"><surname>Voronova</surname><given-names>E. I.</given-names></name></name-alternatives><bio xml:lang="ru"><p>Евгения Ивановна Воронова, кандидат медицинских наук, кафедра психиатрии и психосоматики, ИКМ ФГАОУ ВО Первый МГМУ им. И.М. Сеченова Минздрава России (Сеченовский Университет); ФГБНУ Научный центр психического здоровья</p><p>Москва</p></bio><bio xml:lang="en"><p>Evgeniya I. Voronova, Cand. of Sci. (Med.), Associate Professor, I.M. Sechenov First Moscow State Medical University of the Ministry of Health of the Russian Federation (Sechenov University); FSBSI Mental Health Research Centre</p><p>Moscow</p></bio><email xlink:type="simple">voronova_e@mail.ru</email><xref ref-type="aff" rid="aff-1"/></contrib></contrib-group><aff-alternatives id="aff-1"><aff xml:lang="ru"><institution>ФГБНУ Научный центр психического здоровья;&#13;
ФГАОУ ВО Первый Московский государственный медицинский университет им. И.М. Сеченова Минздрава России (Сеченовский Университет)</institution><country>Россия</country></aff><aff xml:lang="en"><institution>FSBSI Mental Health Research Centre;&#13;
I.M. Sechenov First Moscow State Medical University of the Ministry of Health of the Russian Federation (Sechenov University)</institution><country>Russian Federation</country></aff></aff-alternatives><aff-alternatives id="aff-2"><aff xml:lang="ru"><institution>ФГБНУ Научный центр психического здоровья</institution><country>Россия</country></aff><aff xml:lang="en"><institution>FSBSI Mental Health Research Centre</institution><country>Russian Federation</country></aff></aff-alternatives><pub-date pub-type="collection"><year>2022</year></pub-date><pub-date pub-type="epub"><day>02</day><month>04</month><year>2022</year></pub-date><volume>20</volume><issue>1</issue><fpage>6</fpage><lpage>16</lpage><permissions><copyright-statement>Copyright &amp;#x00A9; Смулевич А.Б., Клюшник Т.П., Борисова П.О., Лобанова В.М., Воронова Е.И., 2022</copyright-statement><copyright-year>2022</copyright-year><copyright-holder xml:lang="ru">Смулевич А.Б., Клюшник Т.П., Борисова П.О., Лобанова В.М., Воронова Е.И.</copyright-holder><copyright-holder xml:lang="en">Smulevich A.B., Klyushnik T.P., Borisova P.O., Lobanova V.M., Voronova E.I.</copyright-holder><license xml:lang="ru" license-type="creative-commons-attribution" xlink:href="https://creativecommons.org/licenses/by/4.0/" xlink:type="simple"><license-p>Данная работа распространяется под лицензией Creative Commons Attribution 4.0.</license-p></license><license xml:lang="en" license-type="creative-commons-attribution" xlink:href="https://creativecommons.org/licenses/by/4.0/" xlink:type="simple"><license-p>This work is licensed under a Creative Commons Attribution 4.0 License.</license-p></license></permissions><self-uri xlink:href="https://www.journalpsychiatry.com/jour/article/view/774">https://www.journalpsychiatry.com/jour/article/view/774</self-uri><abstract><sec><title>Обоснование</title><p>Обоснование: необходимость концептуального осмысления феномена кататонии продиктована новой клинической реальностью. Речь идет о создании на базе данных клинических, нейробиологических, психофармакологических исследований систематики широкого круга кататонических расстройств.</p></sec><sec><title>Цель исследования</title><p>Цель исследования: представить психопатологическую систематику двигательных расстройств, объединенных концепцией кататонии как транснозологического образования (DSM5, проект МКБ-11).</p></sec><sec><title>Пациенты и методы</title><p>Пациенты и методы: обследованы 38 пациентов (20 мужчин, 18 женщин; средний возраст 24,7 года; средняя длительность заболевания 14,4 года), проходивших лечение в отделе по изучению пограничной психиатрии и психосоматических расстройств ФГБНУ «Научный центр психического здоровья» с установленными диагнозами шизофрении (F20), расстройств шизофренического (F21) и шизоаффективного (F25) спектра. Основной критерий включения — наличие в состоянии симптомов непсихотической кататонии. Симптомокомплексы, составляющие психопатологическое пространство кататонической формы шизофрении, т.е. острой психотической кататонии, не рассматриваются.</p></sec><sec><title>Методы исследования</title><p>Методы исследования: клинический, патопсихологический, психометрический, шкала оценки кататонических расстройств (BFCRS), шкала оценки негативных расстройств (SANS).</p></sec><sec><title>Результаты</title><p>Результаты: в ряду категорий двигательных расстройств, объединяющих «непсихотические» формы кататонии, выделено два синдрома — паракинетической (K. Kleist, K. Leonhard) и стереотипной (K. Kleist) кататонии. Паракинетическая кататония характеризуется полиморфизмом двигательных симптомокомплексов с охватом изолированных участков тела, импульсивностью, чрезвычайной интенсивностью, экспрессивностью, эффектом чуждости, потерей произвольности сенсомоторных актов. Эти проявления паракинетической кататонии формируются по механизму психического автоматизма, выступают в качестве трансформеров, видоизменяющих позитивные патопсихологические расстройства и усложняющих клиническую картину последующих эпизодов экзацербации процесса. Симптомокомплексы стереотипной кататонии отличаются однообразием, общей замедленностью, монотонностью двигательных актов, не связанных с ощущением неудобства, чуждости моторных сенсаций. Они формируются по механизму эволюционирующей дискинетопатии и в психопатологическом пространстве заболевания исполняют роль дублеров или амплификаторов таких негативных расстройств, как абулия, пассивность, апатия, эмоциональное уплощение, и когнитивных нарушений. Скованность находится вне сферы внимания пациентов.</p></sec><sec><title>Заключение</title><p>Заключение: выделенные кататонические синдромы — паракинетическая и стереотипная кататония — клинически гетерогенны как в плане путей формирования (механизм психического автоматизма vs эволюционирующая дискинетопатия) и функциональной активности в психопатологическом пространстве заболевания (трансформеры позитивных расстройств vs дублеры негативных изменений), так и клинического прогноза.</p></sec><sec><title> </title><p> </p></sec></abstract><trans-abstract xml:lang="en"><sec><title>Background</title><p>Background: the necessity of conceptual understanding of catatonia phenomenon is dictated by a new clinical reality. The matter concerns creating systematics of a wide range of catatonic disorders, based on the data of clinical, neurobiological and psychopharmacological studies. The aim of the study was to present psychopathological systematics of movement disorders, united by the concept of catatonia as transnosological entity (DSM-5, ICD-11 project).</p></sec><sec><title>Patients and methods</title><p>Patients and methods: a total of 38 patients (20 males; 18 females; mean age 24.7 years; average duration of the disease 14.4 years) were studied. The subjects with established diagnoses of schizophrenia (F20), schizophrenic (F21) and schizoaffective (F25) spectrum disorders underwent treatment in the department of borderline psychiatry and psychosomatic disorders of the FSBSI “Mental Health Research Centre”.</p></sec><sec><title>Methods</title><p>Methods: clinical, pathopsychological, psychometric, Bush Fransis Catatonia Rating Scale (BFCRS), The Scale for the Assessment of Negative Symptoms (SANS).</p></sec><sec><title>Results</title><p>Results: in the range of movement disorders, that combine non-psychotic forms of catatonia, two categories were distinguished, i.e. parakinetic catatonia syndrome (K. Kleist, K. Leonhard) and stereotyped catatonia syndrome (K. Kleist). Manifestations of parakinetic catatonia (polymorphism of motor symptom complexes, covering isolated areas of the body; impulsivity; extreme intensity; expressiveness with the effect of alienation, loss of arbitrariness of sensorimotor acts) are formed according to the mechanism of mental automatism, act as transformers, that modify positive pathocharacterological disorders and complicate the clinical picture of subsequent exacerbations of the process. Symptom complexes of stereotyped catatonia (monotony, general slowness, uniformity of unrelated motor acts/stiffness is out of the scope of patients’ attention/with a feeling of discomfort, alienation of motor sensations) are formed according to the mechanism of evolving dyskinetopathy. In the psychopathology space of the disease they play the role of doublers, amplifiers of negative (abulia, passivity, apathy, emotional fiattening) and cognitive disorders.</p></sec><sec><title>Conclusion</title><p>Conclusion: the identified non-psychotic catatonic syndromes (parakinetic and stereotyped catatonia) are clinically heterogeneous both in terms of the ways of their formation (mechanism of mental automatism/evolving dyskinetopathy) and functional activity in the psychopathology space of the disease (transformers of positive disorders/doublers of negative changes) and clinical prognosis.</p></sec></trans-abstract><kwd-group xml:lang="ru"><kwd>кататония</kwd><kwd>шизофрения</kwd><kwd>психопатология</kwd><kwd>систематика</kwd></kwd-group><kwd-group xml:lang="en"><kwd>catatonia</kwd><kwd>schizophrenia</kwd><kwd>psychopathology</kwd><kwd>systematics</kwd></kwd-group><funding-group><funding-statement xml:lang="ru">При поддержке: грант РФФИ № 19-07-01119 «Интеллектуальный анализ клинических и генетических данных c применением ДСМ-метода автоматизированной поддержки научных исследований дефицитарных изменений при шизофрении и расстройствах шизофренического спектра»</funding-statement><funding-statement xml:lang="en">The work was supported by the Russian Science Foundation, Project # 19-07-01119 "Intellectual analysis of clinical and genetic data using method of automatised support of research in schizophrenia and schizophrenic spectrum disorders"</funding-statement></funding-group></article-meta></front><back><ref-list><title>References</title><ref id="cit1"><label>1</label><citation-alternatives><mixed-citation xml:lang="ru">Tandon R, Heckers S, Bustillo J, Barch DM, Gaebel W, Gur RE, Malaspina D, Owen MJ, Schultz S, Tsuang M, van Os J, Carpenter W. 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